OBJECTIVE: To rare tell to a case of crippling sudden deafness and dizziness due to syndrome of Cogan. CASE REPORT: M.F.F, 75 years, feminine, presented complaint of crippling, uninterrupted vertigo, without triggering factors, followed of nauseas that had started have 11 days. After, it evolved suddenly with deep sensorineural hearing loss to the left, associate the ipsilateral, hyperemia tinnitus and intense pain in region of right cornea. Moreover, patient presented picture of cophosis to the right has 5 years (similar picture to the current one), as well as arthritis history rheumatoid and right chronic osteomyelitis in hallux. To the physical examination, one verified ataxic march, Romberg not carried through due to great instability, interstitial ceratitis in right cornea. The audiometry presented deep sensorineural hearing loss to the left, with low IRF (12% the 100 dB in the 100 monosyllables and 20% dB in disyllables), normal, reflected immittance testing of the absent stapes and cophosis to the right. The otoneurologic examination presented bilateral deficit initial dysfunction of probable which had central etiology to a spontaneous nystagmus alternating with closed eyes. The RNM of skull with emphasis in angle point-cerebelar is normal. Already the laboratorial examinations, the VHS of 36 mm, positive FAN (dotted standard I finish). It was introduced then pentoxifylline, prednisolone in immunosuppressant doses, clonazepan, betahistine, but without therapeutical success, as well as was initiated rehabilitation initial and aural prosthetization, measures these that had finished improving the quality of life of the patient. CONCLUSION: Ahead of a sudden sensorineural loss, associate the cornea alteration anddisabling dizziness, becomes necessary to propose the distinguishing diagnosis of Syndrome of Cogan.