OBJECTIVES: angiodysplasias are vascular anomalies that may or may not show proliferation of the vascular endothelium when they occur are called vascular tumors and subdivided into fragiform hemangioma, tuberous, among others. Vascular bad formations consist of errors of morphogenesis and normal cell cycle and are classified according to the predominant vessel and common occurrence in childhood. It is aimed at reporting a case of malformation of the external ear and the left parotid in a patient treated at the Service of Otolaryngology and correlate with the scientific literature. CASE REPORT: Male patient, 18 years old, sought help with complaints of erythematosus patch left Pinna for 15 years, who developed swelling and deformity of the Pinna ipsilateral pulsatile in the last four years. He denies hearing loss, tinnitus, allergies, and co morbidities. On examination, there was a painless deformity in the left ear, with increase and diffuse hyperemia, mild heat and pulse palpation. Diffuse narrowing of the third external CAE, MT entirety. Right and left otoscopic examination normal. Results angiotomography and arteriography demonstrated that arterial-venous malformation of the ear and infratemporal left parotid region, fed by external carotid branches on this side. Patient in a multidisciplinary approach to medical genetics and vascular surgery in the planning stage for surgical embolization because of episodes of spontaneous bleeding and worsening of picture. CONCLUSION: We sought to highlight a rare presentation of vascular malformation, deformity of the external ear and facial asymmetry and that in this reported case, was exacerbated at puberty, with slowly progressive, requiring intervention.