OBJECTIVE: The lymphoepithelial nasopharyngeal carcinoma is a malignant tumor rarely found in the head and neck, which represents about 1% of all malignancies. Diagnosis is based on clinical history, imaging, and histopathology. Herein, we report the case of a patient with nasopharyngeal lymphoepithelial carcinoma, treated at the department of otorhinolaryngology and cervico-facial surgery of Adriano Jorge Hospital, Manaus-AM. Case Description: The patient, RLE, was a 9-year-old girl, who presented to the ER complaining of a "swollen neck." The examination revealed a cervical tumor, high on the left side of the parotid, accompanied by earache, when he was diagnosed with mumps high and oral antibiotics and analgesia. The patient was hospitalized because her biopsy results were suggestive of lymphoepithelial carcinoma of the nasopharynx. She is currently undergoing chemotherapy. CONCLUSION: Nasopharyngeal carcinoma is highly prevalent in the southern regions of China and linked to infection by the Epstein-Barr virus. This tumor differs significantly from other cancers of the head and neck in terms of its occurrence, causes, clinical behavior, and treatment. Its occurrence in the nasopharynx, neoplasia is rare.